Revascularization of Portal Venous System after Occlusion of Congenital Intrahepatic Portosystemic Shunt


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Figure 1

CTA of the abdomen showing hypoplastic intrahepatic portal branches.

Figure 2

A, Portography before vascular plug placement indicating an IPSS and hypoplastic portal branches. B, The position of the plug confirmed by portography after the operation.

Figure 3

Follow-up CTA at 6 months postoperation demonstrating revascularization of portal venous system.

An 11-month-old boy was admitted to our hospital due to unremitting hyperammonemia. He was diagnosed as having an intrahepatic portosystemic shunt (IPSS) at 24 weeks of gestation. He had no significant symptoms, and physical examination revealed good growth and development. Laboratory results showed an elevated serum ammonia level of 61.6 μmol/L (normal, 0-33 μmol/L), along with normal serum bilirubin and aminotransferase levels.

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